OMIA:002331-9615 : Cardiomyopathy, TNNI3-related in Canis lupus familiaris (dog)

In other species: rabbit

Categories: Cardiovascular system phene

Links to possible relevant human trait(s) and/or gene(s) in OMIM: 613286 (trait) , 115210 (trait) , 613690 (trait) , 611880 (trait) , 191044 (gene)

Single-gene trait/disorder: yes

Mode of inheritance: Autosomal recessive

Disease-related: yes

Key variant known: yes

Year key variant first reported: 2025

Molecular basis: Rivas et al. (2025) investigated hypertrophic cardiomyopathy in Golden Retrievers after "sudden cardiac death of 3 related puppies <2 years of age from 2 dam-offspring repeat matings. ... Whole-genome sequencing "identified a single segregating c.593C>T missense variant in TNNI3 (Cardiac Troponin-I) [omia.variant:1918]. This variant was not observed in the unphenotyped (n=2771) nor in the phenotyped, unrelated cohort of dogs (n=45)."

Breed: Golden Retriever (Dog) (VBO_0200610).
Breeds in which the phene or likely causal variants have been documented. If a likely causal variant has been documented, see variant-specific breed information in the variant table. (Breed information may be incomplete).

Associated gene:

Symbol Description Species Chr Location OMIA gene details page Other Links
TNNI3 troponin I3, cardiac type Canis lupus familiaris 1 NC_051805.1 (103128720..103131893) TNNI3 Ensembl, NCBI gene

Variants

By default, variants are sorted chronologically by year of publication, to provide a historical perspective. Readers can re-sort on any column by clicking on the column header. Click it again to sort in a descending order. To create a multiple-field sort, hold down Shift while clicking on the second, third etc relevant column headers.

WARNING! Inclusion of a variant in this table does not automatically mean that it should be used for DNA testing. Anyone contemplating the use of any of these variants for DNA testing should examine critically the relevant evidence (especially in breeds other than the breed in which the variant was first described). If it is decided to proceed, the location and orientation of the variant sequence should be checked very carefully.

Since October 2021, OMIA includes a semiautomated lift-over pipeline to facilitate updates of genomic positions to a recent reference genome position. These changes to genomic positions are not always reflected in the ‘acknowledgements’ or ‘verbal description’ fields in this table.

OMIA Variant ID Breed(s) Variant Phenotype Gene Allele Variant Type Variant Effect Source of Genetic Variant AVCG Pathogenicity Classification* Reference Sequence Chr. g. or m. c. or n. p. Verbal Description EVA ID Year Published PubMed ID(s) Acknowledgements
1918 Golden Retriever (Dog) Cardiomyopathy, hypertrophic, TNN13-related TNNI3 substitution missense Naturally occurring variant Not currently evaluated UU_Cfam_GSD_1.0 1 NC_049222.1:g.103244333C>T NM_001003041.1:c.593C>T NP_001003041.1:p.(A198V) 2025 40843498

* Variant pathogenicity for single-gene diseases as evaluated according to the Animal Variant Classification Guidelines (AVCG) by the Variant Pathogenicity Working Group of the International Society of Animal Genetics (ISAG) Animal Genetic Testing Standardization (AGTS) Standing Committee: P = pathogenic, LP = likely pathogenic, VUS = variant of unknown significance, LB = likely benign, B = benign. For more information (including details on the classification of each variant) see LINKS.

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Cite this entry

Nicholas, F. W., Tammen, I., & Sydney Informatics Hub. (2026). OMIA:002331-9615: Online Mendelian Inheritance in Animals (OMIA) [dataset]. https://omia.org/. https://doi.org/10.25910/2AMR-PV70

Reference

2025 Rivas, V.N., Goldsmith, D.A., Vandewege, M.W., Li, R.H.L., Losa, S.M., Leber, M., Sitthicharoenchai, P., Hawkes, K., Davies, J.L., Legge, C., Revell, S., Stern, J.A. :
Novel cardiac troponin-I missense variant (c.593C>T) is associated with familial hypertrophic cardiomyopathy in Golden Retrievers. Circ Genom Precis Med 18:e005096, 2025. Pubmed reference: 40843498. DOI: 10.1161/CIRCGEN.125.005096.

Edit History


  • Created by Imke Tammen on 18 Aug 2026
  • Changed by Imke Tammen on 18 Aug 2026